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326default"></div> 327 328 329 330 </li> 331 332 <li class="menu-item menu--one li"> 333 <div class="wrapper"> 334 <span class="trigger"> <a href="/erkrankungen/gicht" data-drupal-link-system-path="node/151">Gicht</a> </span> 335 </div> 336 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 337 338 339 340 </li> 341 </div> 342</ul> 343 344 345 </li> 346 347 <li class="menu-item level--zero menu-item--expanded li"> 348 <div class="wrapper"> 349 <span class="trigger"> 350 <a href="/diagnose-und-therapie/diagnose" data-drupal-link-system-path="node/156">Diagnose und Therapie</a> 351 </span> 352 <div class="arrow-wrapper"> 353 <span class="arrow" role="button" aria-label="Diagnose und Therapie"></span> 354 </div> 355 </div> 356 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 357 358 359<ul class="ul menu--level--one menu-level-1"> 360 <div class="max-width desktop--show"> 361 <h4 class="always-active-menu">Diagnose und Therapie</h4> 362 363 <li class="menu-item menu--one li"> 364 <div class="wrapper"> 365 <span class="trigger"> <a href="/diagnose-und-therapie/diagnose" data-drupal-link-system-path="node/156">Diagnose</a> </span> 366 </div> 367 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 368 369 370 371 </li> 372 373 <li class="menu-item menu--one li"> 374 <div class="wrapper"> 375 <span class="trigger"> <a href="/diagnose-und-therapie/therapie" data-drupal-link-system-path="node/161">Therapie</a> </span> 376 </div> 377 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 378 379 380 381 </li> 382 383 <li class="menu-item menu--one li"> 384 <div class="wrapper"> 385 <span class="trigger"> <a href="/diagnose-und-therapie/was-sie-selbst-tun-koennen" data-drupal-link-system-path="node/166">Was Sie selbst tun können</a> </span> 386 </div> 387 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 388 389 390 391 </li> 392 393 <li class="menu-item menu--one li"> 394 <div class="wrapper"> 395 <span class="trigger"> <a href="/diagnose-und-therapie/fieber-welche-arten-gibt-es-eigentlich" data-drupal-link-system-path="node/171">Fieber â welche Arten gibt's da eigentlich?</a> </span> 396 </div> 397 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 398 399 400 401 </li> 402 </div> 403</ul> 404 405 406 </li> 407 408 <li class="menu-item level--zero menu-item--expanded li"> 409 <div class="wrapper"> 410 <span class="trigger"> 411 <a href="/mehralsnurfieber" data-drupal-link-system-path="node/81">FMF - Mehr als nur Fieber / Ailevi Akdeniz AteÅi</a> 412 </span> 413 <div class="arrow-wrapper"> 414 <span class="arrow" role="button" aria-label="FMF - Mehr als nur Fieber / Ailevi Akdeniz AteÅi"></span> 415 </div> 416 </div> 417 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 418 419 420<ul class="ul menu--level--one menu-level-1"> 421 <div class="max-width desktop--show"> 422 <h4 class="always-active-menu">FMF - Mehr als nur Fieber / Ailevi Akdeniz AteÅi</h4> 423 424 <li class="menu-item menu--one li"> 425 <div class="wrapper"> 426 <span class="trigger"> <a href="/mehralsnurfieber/gamze-senol" data-drupal-link-system-path="node/441">Gamze Senol macht sich stark</a> </span> 427 </div> 428 <div class="menu_link_content menu-link-contentmain view-mode-
428default"></div> 429 430 431 432 </li> 433 </div> 434</ul> 435 436 437 </li> 438 439 <li class="menu-item level--zero menu-item--expanded li"> 440 <div class="wrapper"> 441 <span class="trigger"> 442 <a href="/leben-und-familie" data-drupal-link-system-path="node/36">Leben & Familie</a> 443 </span> 444 <div class="arrow-wrapper"> 445 <span class="arrow" role="button" aria-label="Leben & Familie"></span> 446 </div> 447 </div> 448 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 449 450 451<ul class="ul menu--level--one menu-level-1"> 452 <div class="max-width desktop--show"> 453 <h4 class="always-active-menu">Leben & Familie</h4> 454 455 <li class="menu-item menu--one li"> 456 <div class="wrapper"> 457 <span class="trigger"> <a href="/leben-und-familie/beratung-und-ansprechpartner" data-drupal-link-system-path="node/46">Beratung & Ansprechpartner</a> </span> 458 </div> 459 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 460 461 462 463 </li> 464 465 <li class="menu-item menu--one li"> 466 <div class="wrapper"> 467 <span class="trigger"> <a href="/leben-und-familie/kindergarten-und-schule" data-drupal-link-system-path="node/51">Kindergarten und Schule</a> </span> 468 </div> 469 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 470 471 472 473 </li> 474 475 <li class="menu-item menu--one li"> 476 <div class="wrapper"> 477 <span class="trigger"> <a href="/leben-und-familie/recht-und-soziales" data-drupal-link-system-path="node/56">Recht & Soziales</a> </span> 478 </div> 479 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 480 481 482 483 </li> 484 485 <li class="menu-item menu--one li"> 486 <div class="wrapper"> 487 <span class="trigger"> <a href="/leben-und-familie/reisen" data-drupal-link-system-path="node/61">Reisen</a> </span> 488 </div> 489 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 490 491 492 493 </li> 494 495 <li class="menu-item menu--one li"> 496 <div class="wrapper"> 497 <span class="trigger"> <a href="/leben-und-familie/erwachsen-werden" data-drupal-link-system-path="node/401">Erwachsen werden</a> </span> 498 </div> 499 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 500 501 502 503 </li> 504 505 <li class="menu-item menu--one li"> 506 <div class="wrapper"> 507 <span class="trigger"> <a href="/leben-und-familie/haeufige-fragen" data-drupal-link-system-path="node/66">Häufige Fragen</a> </span> 508 </div> 509 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 510 511 512 513 </li> 514 </div> 515</ul> 516 517 518 </li> 519 520 <li class="menu-item level--zero menu-item--expanded li"> 521 <div class="wrapper"> 522 <span class="trigger"> 523 <a href="/service-und-downloads" data-drupal-link-system-path="node/71">Service & Downloads</a> 524 </span> 525 <div class="arrow-wrapper"> 526 <span class="arrow" role="button" aria-label="Service & Downloads"></span> 527 </div> 528 </div> 529 <div class="menu_link_content menu-link-contentmain view-mode-default"></div> 530 531 532<ul class="ul menu--level--one menu-level-1"> 533 <div class="max-width desktop--show"> 534 <h4 class="always-active-menu">Service & Downloads</h4> 535 536 <li class="menu-item menu--one li"> 537 <div class="wrapper">
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1083 <span class="image--credit p-credits pos-right"> 1084 adobe_stock_236991623_halfpoint 1085 </span> 1086 </div> 1087 </div> 1088<a id="dolphin-banner-bottom-26"><span class="visually-hidden">Bottom of hero banner</span></a> 1089 </div> 1090 1091 </div> 1092</article> 1093 1094 </div> 1095 1096 </section> 1097 1098 <div id="main" class="container-fluid"> 1099 1100 <div class="row content-container clearfix"> 1101 <section class="main-content col-lg-12" id="content" role="main"> 1102 <a id="main-content" tabindex="-1"></a> 1103 1104 1105 1106 <div data-drupal-messages-fallback class="hidden"></div> 1107<div id="block-mainpagecontent" data-block-plugin-id="system_main_block" class="block block-system block-system-main-block block-wrapper"> 1108 1109 1110 1111 1112 1113<article about="/erkrankungen/sjia" class="node node--type-landing-page node--view-mode-full clearfix"> 1114 <div class="node__content mt-0"> 1115 1116 1117 1118 <div class="field field--name-field-page-components field--type-entity-reference-revisions field--label-hidden"> 1119 1120 1121 1122 <div class="field-background-color-none field-banner-overlay-none field-container-background-type-none text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1123 <div class="container"> 1124 1125 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1126 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-one-up"> 1127 <div class="row "> 1128 <div class="col-12"> 1129 1130 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1131 1132 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1133 1134 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1135 <h2 class="brand-primary-text-color">Juveniler Morbus Still: Systemische juvenile idiopathische Arthritis (SJIA)</h2> 1136 </div> 1137 1138 </div> 1139 1140 </div> 1141 1142 <div class="field field--name-field-mobile-slider field--type-boolean field--label-hidden field--layout"> 1143 1144 </div> 1145 1146 </div> 1147 </div> 1148 </div> 1149 1150 </div> 1151 1152 </div> 1153 </div> 1154 1155 1156 1157 1158 <div class="field-background-color-none field-banner-overlay-none field-container-background-type-none text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1159 <div class="container"> 1160 1161 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1162 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-two-up paragraph-text-center-aligned option1"> 1163 <div class="row "> 1164 <div class = "col-12 col-md-6 no-image"> 1165 1166 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1167 1168 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1169 1170 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1171 <p class="neutral-dark-grey-text-color">Hohes Fieber über mindestens 1-2 Schübe pro Tag, geschwollene und schmerzhafte Gelenke: Juveniler Morbus Still ist eine seltene <a href="/erkrankungen/autoinflammatorische-erkrankungen">autoinflammatorische Erkrankung</a>. Sie gehört zu den Rheuma-Erkrankungen und tritt meist bei Kindern im Alter von fünf Jahren oder jünger auf.<sup>1,2,3</sup> Im Gegensatz zu verschiedenen anderen rheumatischen Erkrankungen bei Kindern betrifft juveniler Morbus Still den ganzen Körper und nicht ausschlieÃlich die Gelenke.<sup>7</sup> Morbus Still wird auch âStill-Syndromâ genannt, in der spezifischen, medizinischen Einordnung heiÃt die Erkrankung systemische juvenile idiopathische Arthritis (abgekürzt SJIA). Wenn die Erkrankung bei Erwachsenen erstmals auftritt, wird sie als Morbus Still des Erwachsenen oder <a href="/erkrankungen/aosd">Adult-onset Stillâs Disease</a> (AOSD) bezeichnet.</p> 1172 </div> 1173 1174 </div> 1175 1176 </div> 1177 1178 </div> 1179 <div class = "col-12 col-md-6 image"> 1180 1181 <div class="field field--name-field-layout-2 field--type-entity-reference-revisions field--label-hidden field--layout"> 1182 1183 1184 1185<div class="center gradient-theme-default image--paragraph standard-spacing"> 1186 1187 1188 <div class="field field--name-field-image field--type-entity-reference field--label-hidden"> 1189 1190 1191 1192<picture> 1193 <source data-srcset="/sites/autoinflammation_de/files/styles/twoup_layout_desktop_1080/public/2020-11/grafik-fmf-kinderrheuma-rgb.webp" type="image/webp"> 1194 <img title="Grafik Unterscheidung Kinderrheuma in JIA und SJIA" alt="Grafik Unterscheidung Kinderrheuma in JIA und SJIA" width="1080" height="909" loading="lazy" class="lazyload image-style-twoup-layout-desktop-1080" data-src="/sites/autoinflammation_de/files/styles/twoup_layout_desktop_1080/public/2020-11/grafik-fmf-kinderrheuma-rgb.jpg?itok=vZELHrl-" typeof="foaf:Image" src="data:image/svg+xml;base64,PHN2ZyB4bWxucz0iaHR0cDovL3d3dy53My5vcmcvMjAwMC9zdmciIHZpZXdCb3g9IjAgMCAzIDIiPjwvc3ZnPg==" /> 1195</picture> 1196 1197 1198 1199 </div> 1200 1201 </div> 1202 </div> 1203 1204 </div> 1205 </div> 1206 </div> 1207 1208 </div> 1209 1210 </div> 1211 </div> 1212 1213 1214 1215 1216 <div class="brand-quaternary-light field-banner-overlay-none container-bg--color text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1217 <div class="container"> 1218 1219 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1220 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-two-up paragraph-text-center-aligned option1"> 1221 <div class="row "> 1222 <div class = "col-12 col-md-6 image"> 1223 1224 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1225 1226 1227 1228<div class="center gradient-theme-default image--paragraph standard-spacing pb-35"> 1229 1230 1231 <div class="field field--name-field-image field--type-entity-reference field--label-hidden"> 1232 1233 1234 1235<picture> 1236 <source data-srcset="/sites/autoinflammation_de/files/styles/twoup_layout_desktop_1080/public/2020-11/autoinflammation-sjia-a-rgb.webp" type="image/webp"> 1237 <img title="Ein Junge im Bett mit Fieberthermometer im Mund" alt="Ein Junge im Bett mit Fieberthermometer im Mund" width="1080" height="909" loading="lazy" class="lazyload image-style-twoup-layout-desktop-1080" data-src="/sites/autoinflammation_de/files/styles/twoup_layout_desktop_1080/public/2020-11/autoinflammation-sjia-a-rgb.jpg?itok=ml7arfkF" typeof="foaf:Image" src="data:image/svg+xml;base64,PHN2ZyB4bWxucz0iaHR0cDovL3d3dy53My5vcmcvMjAwMC9zdmciIHZpZXdCb3g9IjAgMCAzIDIiPjwvc3ZnPg==" /> 1238</picture> 1239 1240 1241 1242 </div> 1243 1244 <div class="image--credit neutral-dark-grey-text-color"> 1245 iStock-157589486_heidijpix 1246 </div> 1247 </div> 1248 </div> 1249 1250 </div> 1251 <div class = "col-12 col-md-6 no-image"> 1252 1253 <div class="field field--name-field-layout-2 field--type-entity-reference-revisions field--label-hidden field--layout"> 1254 1255 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1256 1257 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1258 <h3 class="brand-primary-text-color"><strong>Was die medizinische Bezeichnung der Erkrankung bedeutet:</strong></h3><p class="neutral-dark-grey-text-color"><strong>S</strong> = systemisch = die Erkrankung betrifft den ganzen Körper</p><p class="neutral-dark-grey-text-color"><strong>J</strong> = juvenil = die Erkrankung beginnt im Kindesalter</p><p class="neutral-dark-grey-text-color"><strong>I </strong>= idiopathisch = die Ursache ist nicht bekannt</p><p class="neutral-dark-grey-text-color"><strong>A</strong> = Arthritis = Gelenkentzündung</p> 1259 </div> 1260 1261 </div> 1262 1263 </div> 1264 1265 </div> 1266 </div> 1267 </div> 1268 1269 </div> 1270 1271 </div> 1272 </div> 1273 1274 1275 1276 1277 <div class="field-background-color-none field-banner-overlay-none field-container-background-type-none text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1278 <div class="container"> 1279 1280 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1281 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-one-up"> 1282 <div class="row "> 1283 <div class="col-12"> 1284 1285 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1286 1287 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1288 1289 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1290 <h3 class="brand-primary-text-color">Was passiert im Körper bei juvenilem Morbus Still und warum?</h3><p class="neutral-dark-grey-text-color">Der Grund für die auftretenden Beschwerden, also etwa das Fieber und die entzündeten Gelenke, ist eine A
1290ktivierung des angeborenen Immunsystems: Wie bei allen autoinflammatorischen Erkrankungen reagiert es so, als hätte der Körper mit einer Infektion durch Krankheitserreger zu kämpfen. Beim juvenilen Morbus Still spielen hierbei zum Beispiel <a href="/erkrankungen/autoinflammatorische-erkrankungen#immunsystem">Entzündungsbotenstoffe</a> wie Interleukin-1β (IL-1β) und Interleukin-6 (IL-6) eine wichtige Rolle. Auch wenn dies inzwischen erforscht ist, wissen Mediziner bisher nicht, was die Ursache für die Aktivierung des Immunsystems ist. Anders als bei anderen autoinflammatorischen Erkrankungen wie <a href="/erkrankungen/fmf">FMF</a> wurde bislang beispielsweise keine Genveränderung gefunden, den juvenilen Morbus Still verursacht.<sup>2,6</sup></p> 1291 </div> 1292 1293 </div> 1294 1295 </div> 1296 1297 <div class="field field--name-field-mobile-slider field--type-boolean field--label-hidden field--layout"> 1298 1299 </div> 1300 1301 </div> 1302 </div> 1303 </div> 1304 1305 </div> 1306 1307 </div> 1308 </div> 1309 1310 1311 1312 1313 <div class="brand-quaternary-light field-banner-overlay-none container-bg--color text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1314 <div class="container"> 1315 1316 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1317 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-one-up"> 1318 <div class="row "> 1319 <div class="col-12"> 1320 1321 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1322 1323 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1324 1325 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1326 <h2 class="brand-primary-text-color">Juveniler Morbus Still: Welche Symptome auftreten</h2><p class="neutral-dark-grey-text-color">Meist treten bei juvenilem Morbus Still die Symptome als Schub auf, sodass sich gute Phasen mit schlechten abwechseln. Die häufigsten Beschwerden sind wiederkehrende Fieberschübe mit täglichen Spitzen, ein lachsfarbiger Ausschlag auf der Haut und schmerzhafte Gelenkentzündungen. Welche Symptome beim juvenilen Morbus Still während eines akuten Schubs auftreten können, zeigen unsere Ãbersicht und die Grafik:<sup>4,5</sup></p> 1327 </div> 1328 1329 </div> 1330 1331 </div> 1332 1333 <div class="field field--name-field-mobile-slider field--type-boolean field--label-hidden field--layout"> 1334 1335 </div> 1336 1337 </div> 1338 </div> 1339 </div> 1340 1341 </div> 1342 1343 </div> 1344 </div> 1345 1346 1347 1348 1349 <div class="field-background-color-none field-banner-overlay-none field-container-background-type-none text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1350 <div class="container"> 1351 1352 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1353 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-one-up"> 1354 <div class="row "> 1355 <div class="col-12"> 1356 1357 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1358 1359 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1360 1361 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1362 <h3 class="brand-primary-text-color">Mögliche Symptome bei juvenilem Morbus Still (SJIA) im akuten Schub<sup>10</sup></h3> 1363 </div> 1364 1365 </div> 1366 1367 </div> 1368 1369 <div class="field field--name-field-mobile-slider field--type-boolean field--label-hidden field--layout"> 1370 1371 </div> 1372 1373 </div> 1374 </div> 1375 </div> 1376 1377 </div> 1378 1379 </div> 1380 </div> 1381 1382 1383 1384 1385 <div class="field-background-color-none field-banner-overlay-none field-container-background-type-none text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1386 <div class="container"> 1387 1388 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1389 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-two-up paragraph-text-center-aligned option1"> 1390 <div class="row "> 1391 <div class = "col-12 col-md-6 image"> 1392 1393 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1394 1395 1396 1397<div class="center gradient-theme-default image--paragraph standard-spacing"> 1398 1399 1400 <div class="field field--name-field-image field--type-entity-reference field--label-hidden"> 1401 1402 1403 1404<picture> 1405 <source data-srcset="/sites/autoinflammation_de/files/styles/twoup_layout_desktop_1080/public/2020-11/grafik-fmf-sjia-moegliche-symptome-7a-rgb.webp" type="image/webp"> 1406 <img title="Mögliche Symptome bei juvenilem Morbus Still (SJIA) Fieber-Verlauf" alt="Mögliche Symptome bei juvenilem Morbus Still (SJIA) Fieber-Verlauf" width="1080" height="909" loading="lazy" class="lazyload image-style-twoup-layout-desktop-1080" data-src="/sites/autoinflammation_de/files/styles/twoup_layout_desktop_1080/public/2020-11/grafik-fmf-sjia-moegliche-symptome-7a-rgb.jpg?itok=hloZku4X" typeof="foaf:Image" src="data:image/svg+xml;base64,PHN2ZyB4bWxucz0iaHR0cDovL3d3dy53My5vcmcvMjAwMC9zdmciIHZpZXdCb3g9IjAgMCAzIDIiPjwvc3ZnPg==" /> 1407</picture> 1408 1409 1410 1411 </div> 1412 1413 </div> 1414 </div> 1415 1416 </div> 1417 <div class = "col-12 col-md-6 no-image"> 1418 1419 <div class="field field--name-field-layout-2 field--type-entity-reference-revisions field--label-hidden field--layout"> 1420 1421 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1422 1423 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1424 <p class="neutral-dark-grey-text-color">1. Intermittierendes (wiederkehrendes) <a href="/diagnose-und-therapie/fieber-welche-arten-gibt-es-eigentlich">Fieber</a> über mindestens zwei Wochen: Das Fieber bei juvenilem Morbus Still steigt üblicherweise in den frühen Morgenstunden oder am Nachmittag an und sinkt zwischendurch wieder.</p><p class="neutral-dark-grey-text-color">
14242. Flüchtiger Hautausschlag: Lachsfarbige âFleckenâ, die schnell wieder verschwinden können.</p><p class="neutral-dark-grey-text-color">3. Geschwollene und schmerzende Gelenke: Bei einigen Kindern mit juvenilem Morbus Still treten zuerst Fieber und Ausschlag auf, die Gelenkentzündung (Arthritis) kommt später dazu. Manche Kinder haben während des Fiebers nur allgemeine Muskel- oder Gelenkschmerzen, oft ohne sichtbare Gelenkschwellungen. Die inneren Organe können mit betroffen sein: Lymphknoten, Leber und Milz sind oft vergröÃert.</p> 1425 </div> 1426 1427 </div> 1428 1429 </div> 1430 1431 </div> 1432 </div> 1433 </div> 1434 1435 </div> 1436 1437 </div> 1438 </div> 1439 1440 1441 1442 1443 <div class="brand-quaternary-light field-banner-overlay-none container-bg--color text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1444 <div class="container"> 1445 1446 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1447 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-two-up paragraph-text-center-aligned option1"> 1448 <div class="row "> 1449 <div class = "col-12 col-md-6 no-image"> 1450 1451 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1452 1453 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1454 1455 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1456 <p class="neutral-dark-grey-text-color"><strong>1. Zentrales Nervensystem:</strong></p><p class="neutral-dark-grey-text-color">Selten betroffen</p><p class="neutral-dark-grey-text-color"><strong>2. Herz:</strong></p><p class="neutral-dark-grey-text-color">Entzündung</p><p class="neutral-dark-grey-text-color"><strong>3. Lymphsystem und Milz:</strong></p><p class="neutral-dark-grey-text-color">VergröÃerung von Lymphknoten und/oder Milz</p><p class="neutral-dark-grey-text-color"><strong>4. Leber:</strong></p><p class="neutral-dark-grey-text-color">VergröÃerung der Leber seltener als VergröÃerung der Milz</p><p class="neutral-dark-grey-text-color"><strong>5. Lunge:</strong></p><p class="neutral-dark-grey-text-color">Selten betroffen</p><p class="neutral-dark-grey-text-color"><strong>6. Muskeln und Knochen:</strong></p><p class="neutral-dark-grey-text-color">Gelenkentzündung (Arthritis)<br>Sehnenscheidenentzündung<br>Muskelschmerzen</p> 1457 </div> 1458 1459 </div> 1460 1461 </div> 1462 1463 </div> 1464 <div class = "col-12 col-md-6 image"> 1465 1466 <div class="field field--name-field-layout-2 field--type-entity-reference-revisions field--label-hidden field--layout"> 1467 1468 1469 1470<div class="center gradient-theme-default image--paragraph standard-spacing"> 1471 1472 1473 <div class="field field--name-field-image field--type-entity-reference field--label-hidden"> 1474 1475 1476 1477<picture> 1478 <source data-srcset="/sites/autoinflammation_de/files/styles/twoup_layout_desktop_1080/public/2020-11/grafik-fmf-sjia-moegliche-symptome-7c-rgb.webp" type="image/webp"> 1479 <img title="Mögliche Symptome bei juvenilem Morbus Still (SJIA) nummerierte Grafik" alt="Mögliche Symptome bei juvenilem Morbus Still (SJIA) nummerierte Grafik" width="1080" height="909" loading="lazy" class="lazyload image-style-twoup-layout-desktop-1080" data-src="/sites/autoinflammation_de/files/styles/twoup_layout_desktop_1080/public/2020-11/grafik-fmf-sjia-moegliche-symptome-7c-rgb.jpg?itok=bOtRuYCs" typeof="foaf:Image" src="data:image/svg+xml;base64,PHN2ZyB4bWxucz0iaHR0cDovL3d3dy53My5vcmcvMjAwMC9zdmciIHZpZXdCb3g9IjAgMCAzIDIiPjwvc3ZnPg==" /> 1480</picture> 1481 1482 1483 1484 </div> 1485 1486 </div> 1487 </div> 1488 1489 </div> 1490 </div> 1491 </div> 1492 1493 </div> 1494 1495 </div> 1496 </div> 1497 1498 1499 1500 1501 <div class="gradient-primary-left use-padding-defaults"> 1502 <div class="field-background-color-none field-banner-overlay-none container-bg--gradient text-theme-light gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1503 <div class="container"> 1504 1505 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1506 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-two-up option1"> 1507 <div class="row "> 1508 <div class = "col-12 col-md-6 no-image"> 1509 1510 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1511 1512 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1513 1514 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1515 <h3 class="neutral-white-text-color"><a class="ck-anchor" id="ada">Symptom-Check mit Ada</a></h3><p class="neutral-white-text-color">Der Symptom-Check basiert auf der von Wissenschaftlern und Medizinern entwickelten Gesundheits-App âAdaâ.</p><p class="neutral-white-text-color">Alle Symptome werden ganz genau abgefragt. Daraus wird abgeleitet, welche Erkrankung man möglicherweise haben könnte.</p><p class="neutral-white-text-color">Gerade bei einer seltenen Erkrankung wie dem familiären Mittelmeerfieber kann der Symptom-Check mit Ada sehr hilfreich sein.</p> 1516 </div> 1517 1518 </div> 1519 1520 1521 <div class="gradient-theme-default paragraph paragraph--type--button"> 1522 1523 1524 <div class="field field--name-field-button-link field--type-link field--label-hidden"> 1525
1526 <a class="launch-ada button primary button--left button--primary brand-accent-button brand-accent-border-button border-width-0 white-no-transition-text" href="">Zum Symptom-Check</a> 1527 </div> 1528 1529 </div> 1530 1531 1532 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1533 1534 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1535 <p class="neutral-white-text-color"><sup>Diese web-basierte Anwendung zur persönlichen Symptomanalyse wird Ihnen von der Ada Health GmbH ("Ada") zur Verfügung gestellt. Die Datenverarbeitung ihrer personenbezogenen Daten erfolgt ausschlieÃlich bei Ada als verantwortliche Stelle im Sinne der DSGVO. Novartis hat keinen Zugriff auf Ihre personenbezogenen Daten oder die Ergebnisse Ihrer Symptomanalyse.</sup></p> 1536 </div> 1537 1538 </div> 1539 1540 </div> 1541 1542 </div> 1543 <div class = "col-12 col-md-6 image"> 1544 1545 <div class="field field--name-field-layout-2 field--type-entity-reference-revisions field--label-hidden field--layout"> 1546 1547 1548 1549<div class="center gradient-theme-default image--paragraph standard-spacing pb-35"> 1550 1551 1552 <div class="field field--name-field-image field--type-entity-reference field--label-hidden"> 1553 1554 1555 1556<picture> 1557 <source data-srcset="/sites/autoinflammation_de/files/styles/twoup_layout_desktop_1080/public/2021-03/ada-novartis-760x640.webp" type="image/webp"> 1558 <img title="Tablet mit der ADA App und Logo" alt="Tablet mit der ADA App und Logo" width="1080" height="909" loading="lazy" class="lazyload image-style-twoup-layout-desktop-1080" data-src="/sites/autoinflammation_de/files/styles/twoup_layout_desktop_1080/public/2021-03/ada-novartis-760x640.jpg?itok=y2nk2Phf" typeof="foaf:Image" src="data:image/svg+xml;base64,PHN2ZyB4bWxucz0iaHR0cDovL3d3dy53My5vcmcvMjAwMC9zdmciIHZpZXdCb3g9IjAgMCAzIDIiPjwvc3ZnPg==" /> 1559</picture> 1560 1561 1562 1563 </div> 1564 1565 <div class="image--credit neutral-white-text-color"> 1566 Ada Health GmbH 1567 </div> 1568 </div> 1569 </div> 1570 1571 </div> 1572 </div> 1573 </div> 1574 1575 </div> 1576 1577 </div> 1578 </div> 1579 </div> 1580 1581 1582 1583 1584 <div class="field-background-color-none field-banner-overlay-none field-container-background-type-none text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1585 <div class="container"> 1586 1587 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1588 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-one-up"> 1589 <div class="row "> 1590 <div class="col-12"> 1591 1592 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1593 1594 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1595 1596 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1597 <h3 class="brand-primary-text-color"><strong>Juveniler Morbus Still: Warum die Diagnostik oft langwierig ist</strong></h3><p class="neutral-dark-grey-text-color">Wenn ein Kind immer wieder unter wochenlangem Fieber und Gelenkschmerzen leidet, möchten Eltern endlich wissen, was die Ursache dafür ist. Mit der richtigen Diagnose kann auch die zielgerichtete <a href="#therapie">Therapie</a> begonnen werden.</p><p class="neutral-dark-grey-text-color">Leider dauert es bei juvenilem Morbus Still wie bei vielen autoinflammatorischen Erkrankungen oft lange, bis die <a href="/diagnose-und-therapie/diagnose">richtige Diagnose</a> gefunden ist. Während eines akuten Schubs ist die Erkrankung leichter feststellbar als in einer symptomfreien Phase. Deshalb ist es wichtig, gerade während eines Schubs möglichst einen <a href="/service-und-downloads/spezialistensuche">Spezialisten</a> für Kinder-Rheumatologie aufzusuchen.</p><p class="neutral-dark-grey-text-color">Um die Diagnose juveniler Morbus Still zu stellen, wird der Arzt für die Diagnostik neben einer körperlichen Untersuchung weitere Untersuchungen anordnen, etwa der Gelenke oder inneren Organe. Hinzu kommt meist eine Kontrolle der Blutwerte. Bei juvenilem Morbus Still werden beispielsweise folgende Laborwerte erhoben:<sup>6</sup></p><ul><li class="neutral-dark-grey-text-color">Parameter zur Feststellung einer erhöhten Entzündungsaktivität bei juvenilem Morbus Still wie <a href="/diagnose-und-therapie/diagnose">C-reaktives Protein (CRP), die Blutsenkungsgeschwindigkeit (BSG), Leukozyten oder Ferritin</a>.</li><li class="neutral-dark-grey-text-color">Spezifische Auto-Antikörper, um andere Erkrankungen auszuschlieÃen.</li></ul> 1598 </div> 1599 1600 </div> 1601 1602 </div> 1603 1604 <div class="field field--name-field-mobile-slider field--type-boolean field--label-hidden field--layout"> 1605 1606 </div> 1607 1608 </div> 1609 </div> 1610 </div> 1611 1612 </div> 1613 1614 </div> 1615 </div> 1616 1617 1618 1619 1620 <div class="brand-quaternary-light field-banner-overlay-none container-bg--color text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1621 <div class="container"> 1622 1623 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1624 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-two-up option1"> 1625 <div class="row "> 1626 <div class = "col-12 col-md-6 image"> 1627 1628 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1629 1630 1631 1632<div class="center gradient-theme-default image--paragraph standard-spacing pb-35"> 1633 1634 1635 <div class="field field--name-field-image field--type-entity-reference field--label-hidden"> 1636 1637 1638 1639<picture> 1640 <source data-srcset="/sites/autoinflammation_de/files/styles/twoup_layout_desktop_1080/public/2023-03/juveniler-morbus-still.webp" type="image/webp"> 1641 <img alt="Artzgespräch" width="1080" height="909" loading="lazy" class="lazyload image-style-twoup-layout-desktop-1080" data-src="/sites/autoinflammation_de/files/styles/twoup_layout_desktop_1080/public/2023-03/juveniler-morbus-still.jpg?itok=_m0weSpO" typeof="foaf:Image" src="data:image/svg+xml;base64,PHN2ZyB4bWxucz0iaHR0cDovL3d3dy53My5vcmcvMjAwMC9zdmciIHZpZXdCb3g9IjAgMCAzIDIiPjwvc3ZnPg==" /> 1642</picture> 1643 1644 1645 1646 </div> 1647 1648 <div class="image--credit neutral-dark-grey-text-color"> 1649 iStock, 1148334988, andrei_r 1650 </div> 1651 </div> 1652 </div> 1653 1654 </div> 1655 <div class = "col-12 col-md-6 no-image"> 1656 1657 <div class="field field--name-field-layout-2 field--type-entity-reference-revisions field--label-hidden field--layout"> 1658 1659 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1660 1661 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1662 <h3 class="brand-primary-text-color"><a class="ck-anchor" id="therapie">Juveniler Morbus Still: Die Therapie</a></h3><p class="neutral-dark-grey-text-color">Steht die Diagnose juveniler Morbus Still fest, kann der Arzt mit der passenden Behandlung beginnen. Diese ist nicht nur wichtig, um die Anzahl und Schwere der Schübe zu reduzieren, sondern auch, um mögliche Spätfolgen wie eine Amyloidose zu verhindern.<sup>2</sup></p><p class="neutral-dark-grey-text-color">Während eines akuten Schubs können <a href="/diagnose-und-therapie/therapie#wirkstoffe">schmerzlindernde, entzündungshemmende und fiebersenkende Wirkstoffe </a>die Symptome lindern. Ist ein akuter Schub sehr stark, lassen sich Glukokortikoide (Kortison) einsetzen, allerdings s
1662ollte eine längerfristige Therapie damit vermieden werden.</p><p class="neutral-dark-grey-text-color">Sogenannte <a href="/diagnose-und-therapie/therapie#wirkstoffe">Biologika </a>können die vermehrt ausgeschütteten Entzündungsbotenstoffe reduzieren und so die Entzündung im Körper regulieren helfen.<sup>6,8,9</sup></p> 1663 </div> 1664 1665 </div> 1666 1667 </div> 1668 1669 </div> 1670 </div> 1671 </div> 1672 1673 </div> 1674 1675 </div> 1676 </div> 1677 1678 1679 1680 1681 <div class="field-background-color-none field-banner-overlay-none field-container-background-type-none text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1682 <div class="container"> 1683 1684 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1685 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-one-up"> 1686 <div class="row "> 1687 <div class="col-12"> 1688 1689 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1690 1691 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1692 1693 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1694 <h3 class="brand-primary-text-color"><strong>Juveniler Morbus Still: Was Sie über den Verlauf und mögliche Spätfolgen wissen sollten</strong></h3><p class="neutral-dark-grey-text-color">Die Krankheit kann bei verschiedenen Kindern ganz unterschiedlich verlaufen (auch das macht die Diagnosestellung schwierig).</p> 1695 </div> 1696 1697 </div> 1698 1699 </div> 1700 1701 <div class="field field--name-field-mobile-slider field--type-boolean field--label-hidden field--layout"> 1702 1703 </div> 1704 1705 </div> 1706 </div> 1707 </div> 1708 1709 </div> 1710 1711 </div> 1712 </div> 1713 1714 1715 1716 1717 <div class="brand-quaternary-light field-banner-overlay-none container-bg--color text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1718 <div class="container"> 1719 1720 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1721 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-two-up paragraph-text-center-aligned option1"> 1722 <div class="row "> 1723 <div class = "col-12 col-md-6 no-image"> 1724 1725 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1726 1727 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1728 1729 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1730 <p class="neutral-dark-grey-text-color">Mögliche Krankheitsverläufe bei Morbus Still (SJIA)<sup>2,16,17</sup></p><ul><li class="neutral-dark-grey-text-color">Es gibt Kinder, für die ist ein Morbus Still-Schub ein einmaliges Ereignis, man spricht dann von monozyklisch.</li><li class="neutral-dark-grey-text-color">Manche Kinder haben jedoch immer wieder Schübe, man spricht von polyzyklisch. Meist tritt hierbei nur eine leichte Gelenkentzündung auf.</li><li class="neutral-dark-grey-text-color">Ein Teil der Kinder hat eine anhaltende, immer aktive Erkrankung (chronisch, persistent). Dies ist die häufigste Form von Morbus Still (SJIA).</li></ul> 1731 </div> 1732 1733 </div> 1734 1735 </div> 1736 1737 </div> 1738 <div class = "col-12 col-md-6 image"> 1739 1740 <div class="field field--name-field-layout-2 field--type-entity-reference-revisions field--label-hidden field--layout"> 1741 1742 1743 1744<div class="center gradient-theme-default image--paragraph standard-spacing"> 1745 1746 1747 <div class="field field--name-field-image field--type-entity-reference field--label-hidden"> 1748 1749 1750 1751<picture> 1752 <source data-srcset="/sites/autoinflammation_de/files/styles/twoup_layout_desktop_1080/public/2020-11/grafik-fmf-sjia-krankheitsverlauf-a-rgb.webp" type="image/webp"> 1753 <img title="Krankheitsverlauf bei juvenilem Morbus Still (SJIA)" alt="Krankheitsverlauf bei juvenilem Morbus Still (SJIA)" width="1080" height="909" loading="lazy" class="lazyload image-style-twoup-layout-desktop-1080" data-src="/sites/autoinflammation_de/files/styles/twoup_layout_desktop_1080/public/2020-11/grafik-fmf-sjia-krankheitsverlauf-a-rgb.jpg?itok=reX8OLLs" typeof="foaf:Image" src="data:image/svg+xml;base64,PHN2ZyB4bWxucz0iaHR0cDovL3d3dy53My5vcmcvMjAwMC9zdmciIHZpZXdCb3g9IjAgMCAzIDIiPjwvc3ZnPg==" /> 1754</picture> 1755 1756 1757 1758 </div> 1759 1760 </div> 1761 </div> 1762 1763 </div> 1764 </div> 1765 </div> 1766 1767 </div> 1768 1769 </div> 1770 </div> 1771 1772 1773 1774 1775 <div class="field-background-color-none field-banner-overlay-none field-container-background-type-none text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1776 <div class="container"> 1777 1778 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1779 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-one-up"> 1780 <div class="row "> 1781 <div class="col-12"> 1782 1783 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1784 1785 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1786 1787 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1788 <h3 class="brand-primary-text-color"><a class="ck-anchor" id="folgen">Aufgrund der Aktivierung des unspezifischen Immunsystems kann es bei juvenilem Morbus Still zu folgenden Spätfolgen und Komplikationen kommen:</a></h3><ul><li class="neutral-dark-grey-text-color"><strong>Amyloidose:</strong> Durch die fortwährende Entzündung im Körper ist im Blut ständig die Anzahl der Akute-Phase-Proteine erhöht, die normalerweise die Entzündung regulieren. Im Laufe der Erkrankung lagert sich ein bestimmtes Akute-Phase-Protein, das Serum-Amyloid-A (SAA), im Nierengewebe ab. Das nennt man Amyloidose, die zur Schädigung der Nieren führen kann. Dank verbesserter Diagnostik und Behandlung sind die Amyloidose und das durch sie verursachte chronische Nierenversagen seltener geworden.</li><li class="neutral-dark-grey-text-color"><strong>Gelenkzerstörung:</strong> Im langfristigen Verlauf kann die schubweise Gelenkentzündung in eine dauerhafte Entzündung, die die Gelenke zerstört, übergehen. Dies wird als chronisch destruktive Arthritis bezeichnet. Eine frühzeitige, effektive Behandlung kann dieser möglichen Spätfolge entgegenwirken.<sup>4,5,6</sup></li><li class="neutral-dark-grey-text-color"><strong>Weitere Langzeitfolgen: </strong>Im weiteren Verlauf können bei juvenilem Morbus Still zudem Funktionseinschränkungen der Gelenke und eine Wachstumsverminderung auftreten.<sup>4,5</sup> Etwa 41 Prozent der SJIA-Patienten haben im Vergleich zu Gesunden eine geringere KörpergröÃe.<sup>11</sup></li><li class="neutral-dark-grey-text-color"><strong>Makrophagenaktivierungssyndrom (MAS):</strong> Eine schwere Komplikation, die bei etwa 10 Prozent der Patienten mit juvenilem Morbus-Still auftritt.<sup>5,12-14</sup> Die Ursache ist eine zu starke Aktivierung des Immunsystems. Dadurch kann es zu Beschwerden wie bei einer Blutvergiftung (Sepsis) kommen â bis hin zum Versagen verschiedener innerer Organe.<sup>12, 15</sup></li></ul> 1789 </div> 1790 1791 </div> 1792 1793 </div> 1794 1795 <div class="field field--name-field-mobile-slider field--type-boolean field--label-hidden field--layout"> 1796 1797 </div> 1798 1799 </div> 1800 </div> 1801 </div> 1802 1803 </div> 1804 1805 </div> 1806 </div> 1807 1808 1809 1810 1811 <div class="brand-quaternary-light field-banner-overlay-none container-bg--color text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1812 <div class="container"> 1813 1814 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1815 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-one-up"> 1816 <div class="row "> 1817 <div class="col-12"> 1818 1819 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1820 1821 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1822 1823 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1824 <h2 class="text-align-center brand-primary-text-color">Das könnte Sie auch interessieren:</h2> 1825 </div> 1826 1827 </div> 1828 1829 </div> 1830 1831 <div class="field field--name-field-mobile-slider field--type-boolean field--label-hidden field--layout"> 1832 1833 </div> 1834 1835 </div> 1836 </div> 1837 </div> 1838 1839 </div> 1840 1841 </div> 1842 </div> 1843 1844 1845 1846 1847 <div class="brand-quaternary-light field-banner-overlay-none container-bg--color text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 1848 <div class="container"> 1849 1850 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 1851 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-three-up"> 1852 <div class="row "> 1853 <div class="col-12 col-md-4"> 1854 1855 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 1856 1857 1858 1859<div class="center gradient-theme-default image--paragraph standard-spacing pb-35"> 1860 1861 1862 <div class="field field--name-field-image field--type-entity-reference field--label-hidden"> 1863 1864 1865 1866<picture> 1867 <source data-srcset="/sites/autoinflammation_de/files/styles/threeup_layout_desktop_700/public/2021-03/ada-novartis-760x640.webp" type="image/webp"> 1868 <img title="Tablet mit der ADA App und Logo" alt="Tablet mit der ADA App und Logo" width="700" height="589" loading="lazy" class="lazyload image-style-threeup-layout-desktop-700" data-src="/sites/autoinflammation_de/files/styles/threeup_layout_desktop_700/public/2021-03/ada-novartis-760x640.jpg?itok=NDM4Hk2k" typeof="foaf:Image" src="data:image/svg+xml;base64,PHN2ZyB4bWxucz0iaHR0cDovL3d3dy53My5vcmcvMjAwMC9zdmciIHZpZXdCb3g9IjAgMCAzIDIiPjwvc3ZnPg==" /> 1869</picture> 1870 1871 1872 1873 </div> 1874 1875 <div class="image--credit neutral-dark-grey-text-color"> 1876 Ada Health GmbH 1877 </div> 1878 </div> 1879 1880 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1881 1882 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1883 <h3 class="text-align-center brand-primary-text-color">Symptom-Check mit Ada</h3> 1884 </div> 1885 1886 </div> 1887 1888 1889 <div class="gradient-theme-default paragraph paragraph--type--button"> 1890 1891 1892 <div class="field field--name-field-button-link field--type-link field--label-hidden"> 1893 1894 <a class="button primary button--center button--primary brand-accent-button brand-accent-border-button border-width-0 white-no-transition-text" href="#ada">Zum Symptom-Check</a> 1895 </div> 1896 1897 </div> 1898 1899 </div> 1900 1901 </div> 1902 <div class="col-12 col-md-4"> 1903 1904 <div class="field field--name-field-layout-2 field--type-entity-reference-revisions field--label-hidden field--layout"> 1905 1906 1907 1908<div class="center gradient-theme-default image--paragraph standard-spacing pb-35"> 1909 1910 1911 <div class="field field--name-field-image field--type-entity-reference field--label-hidden"> 1912 1913 1914 1915<picture> 1916 <source data-srcset="/sites/autoinflammation_de/files/styles/threeup_layout_desktop_700/public/2021-06/autoinflammation-diagnose-b-0-rgb_0.webp" type="image/webp"> 1917 <img title="Stethoskop und Notizblock" alt="Stethoskop und Notizblock" width="700" height="589" loading="lazy" class="lazyload image-style-threeup-layout-desktop-700" data-src="/sites/autoinflammation_de/files/styles/threeup_layout_desktop_700/public/2021-06/autoinflammation-diagnose-b-0-rgb_0.jpg?itok=WvYH16Vl" typeof="foaf:Image" src="data:image/svg+xml;base64,PHN2ZyB4bWxucz0iaHR0cDovL3d3dy53My5vcmcvMjAwMC9zdmciIHZpZXdCb3g9IjAgMCAzIDIiPjwvc3ZnPg==" /> 1918</picture> 1919 1920 1921 1922 </div> 1923 1924 <div class="image--credit neutral-dark-grey-text-color"> 1925 iStock-1098340172_12963734 1926 </div> 1927 </div> 1928 1929 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1930 1931 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1932 <h3 class="text-align-center brand-primary-text-color">Diagnose</h3> 1933 </div> 1934 1935 </div> 1936 1937 1938 <div class="gradient-theme-default paragraph paragraph--type--button"> 1939 1940 1941 <div class="field field--name-field-button-link field--type-link field--label-hidden"> 1942 1943 <a class="button primary button--center button--primary brand-accent-button brand-accent-border-button border-width-0 white-no-transition-text" href="/diagnose-und-therapie/diagnose">Mehr erfahren</a> 1944 </div> 1945 1946 </div> 1947 1948 </div> 1949 1950 </div> 1951 <div class="col-12 col-md-4"> 1952 1953 <div class="field field--name-field-layout-3 field--type-entity-reference-revisions field--label-hidden field--layout"> 1954 1955 1956 1957<div class="center gradient-theme-default image--paragraph standard-spacing pb-35"> 1958 1959 1960 <div class="field field--name-field-image field--type-entity-reference field--label-hidden"> 1961 1962 1963 1964<picture> 1965 <source data-srcset="/sites/autoinflammation_de/files/styles/threeup_layout_desktop_700/public/2021-06/autoinflammation-links-und-downloads-b-rgb.webp" type="image/webp"> 1966 <img title="Vater mit seinem Sohn schaut auf einen Laptop und lacht" alt="Vater mit seinem Sohn schaut auf einen Laptop und lacht" width="700" height="589" loading="lazy" class="lazyload image-style-three
1966up-layout-desktop-700" data-src="/sites/autoinflammation_de/files/styles/threeup_layout_desktop_700/public/2021-06/autoinflammation-links-und-downloads-b-rgb.jpg?itok=v6HfZgFv" typeof="foaf:Image" src="data:image/svg+xml;base64,PHN2ZyB4bWxucz0iaHR0cDovL3d3dy53My5vcmcvMjAwMC9zdmciIHZpZXdCb3g9IjAgMCAzIDIiPjwvc3ZnPg==" /> 1967</picture> 1968 1969 1970 1971 </div> 1972 1973 <div class="image--credit neutral-dark-grey-text-color"> 1974 iStock-807364128_monkeybusinessimages 1975 </div> 1976 </div> 1977 1978 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 1979 1980 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 1981 <h3 class="text-align-center brand-primary-text-color">Videointerviews</h3> 1982 </div> 1983 1984 </div> 1985 1986 1987 <div class="gradient-theme-default paragraph paragraph--type--button"> 1988 1989 1990 <div class="field field--name-field-button-link field--type-link field--label-hidden"> 1991 1992 <a class="button primary button--center button--primary brand-accent-button brand-accent-border-button border-width-0 white-no-transition-text" href="/service-und-downloads/videos">Zu den Videos</a> 1993 </div> 1994 1995 </div> 1996 1997 </div> 1998 1999 </div> 2000 </div> 2001 </div> 2002 2003 </div> 2004 2005 </div> 2006 </div> 2007 2008 2009 2010 2011 <div class="field-background-color-none field-banner-overlay-none field-container-background-type-none text-theme-default gradient-theme-default paragraph--view-mode--default paragraph paragraph--type--content-container use-padding-defaults" data-less_576=1.875 data-great_576=1.875 data-great_768=1.875 data-great_992=1.875 data-great_1200=1.875> 2012 <div class="container"> 2013 2014 <div class="field field--name-field-items field--type-entity-reference-revisions field--label-hidden"> 2015 <div class="gradient-theme-default paragraph paragraph-layout paragraph--type--layout-one-up"> 2016 <div class="row "> 2017 <div class="col-12"> 2018 2019 <div class="field field--name-field-layout-1 field--type-entity-reference-revisions field--label-hidden field--layout"> 2020 2021 <div class="gradient-theme-default paragraph paragraph--type--simple-text"> 2022 2023 <div class="clearfix text-formatted field field--name-field-content field--type-text-long field--label-hidden"> 2024 <p class="neutral-dark-grey-text-color"><strong>Quellen:</strong></p><ol><li class="neutral-dark-grey-text-color">Dinarello CA: Blocking IL-1 in systemic inflammation. DOI: <a class="id-link" href="https://doi.org/10.1084/jem.20050640" target="_blank" rel="noopener">10.1084/jem.20050640</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Woo P: Systemic juvenile idiopathic arthritis: diagnosis, management, and outcome. DOI: <a class="id-link" href="https://translate.google.com/website?sl=en&tl=de&hl=de&prev=search&u=https://doi.org/10.1038/ncprheum0084" target="_blank" rel="noopener">10.1038/ncprheum0084</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Behrens EM, Beukelman T, Gallo L et al.: Evaluation of the presentation of systemic onset juvenile rheumatoid arthritis: data from the Pennsylvania Systemic Onset Juvenile Arthritis Registry (PASOJAR). <a href="https://www.jrheum.org/content/35/2/343.long">https://www.jrheum.org/content/35/2/343.long</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Cassidy JT, Petty RE, Laxer RM, et al.: <a href="https://books.google.de/books/about/Textbook_of_Pediatric_Rheumatology_E_Boo.html?id=oEemcpeEufoC&redir_esc=y">Textbook of Pediatric Rheumatology</a>. 6th ed. Philadelphia, PA: Saunders Elsevier; 2011; 236â47.</li><li class="neutral-dark-grey-text-color">Ravelli A, Martini A: Juvenile idiopathic arthritis. DOI: <a class="id-l
2024ink" href="https://doi.org/10.1016/s0140-6736(07)60363-8" target="_blank" rel="noopener">10.1016/S0140-6736(07)60363-8</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Hinze, C., Holzinger, D.: Harmonisierung der Diagnostik und Therapie der systemischen juvenilen Arthtritis in Deutschland. DOI: <a href="https://www.thieme-connect.de/products/ejournals/abstract/10.1055/s-0037-1618435">10.1055/s-0037-1618435</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Ramanan AV, Grom AA: Does systemic-onset juvenile idiopathic arthritis belong under juvenile idiopathic arthritis? DOI: <a class="id-link" href="https://doi.org/10.1093/rheumatology/keh710" target="_blank" rel="noopener">10.1093/rheumatology/keh710</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Beukelman T, Patkar NM, Saag KG, et al.: 2011 American College of Rheumatology Recommendations for the Treatment of Juvenile Idiopathic Arthritis: Initiation and Safety Monitoring of Therapeutic Agents for the Treatment of Arthritis and Systemic Features. DOI: <a class="id-link" href="https://doi.org/10.1002/acr.20460" target="_blank" rel="noopener">10.1002/acr.20460</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Dewitt EM, Kimura Y, Beukelman T, et al.: Consensus Treatment Plans for New-Onset Systemic Juvenile Idiopathic Arthritis. DOI: <a class="id-link" href="https://doi.org/10.1002/acr.21625" target="_blank" rel="noopener">10.1002/acr.21625</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Frosch M, Roth J: New insights in systemic juvenile idiopathic arthritis-from pathophysiology to treatment. DOI: <a class="id-link" href="https://doi.org/10.1093/rheumatology/kem271" target="_blank" rel="noopener">10.1093/rheumatology/kem271</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Simon D, Lucidarme N, Prieur AM et al.: Treatment of growth failure in juvenile chronic arthritis. DOI: <a class="id-link" href="https://pubmed.ncbi.nlm.nih.gov/12373011/" target="_blank" rel="noopener">10.1159/000064770</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Weiss JE, Ilowite NT: Juvenile idiopathic arthritis. DOI: <a class="id-link" href="https://doi.org/10.1016/j.pcl.2005.01.007" target="_blank" rel="noopener">10.1016/j.pcl.2005.01.007</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Sawhney S, Woo P, Murray K: Macrophage activation syndrome: a potentially fatal complication of rheumatic disorders. DOI: <a class="id-link" href="https://doi.org/10.1136/adc.85.5.421" target="_blank" rel="noopener">10.1136/adc.85.5.421</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Stéphan JL, Koné-Paut I, Galambrun C et al.: Reactive Haemophagocytic syndrome in children with inflammatory disorders. A retrospective study of 24 patients. DOI: <a class="id-link" href="https://doi.org/10.1093/rheumatology/40.11.1285" target="_blank" rel="noopener">10.1093/rheumatology/40.11.1285</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Kelly A, Ramanan AV: Recognition and management of macrophage activation syndrome in juvenile arthritis. DOI: <a class="id-link" href="https://doi.org/10.1097/bor.0b013e32825a6a79" target="_blank" rel="noopener">10.1097/BOR.0b013e32825a6a79</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Mellins ED, Macaubas C, Grom AA: Pathogenesis of systemic juvenile idiopathic arthritis: some answers, more questions. DOI: <a class="id-link" href="https://doi.org/10.1038/nrrheum.2011.68" target="_blank" rel="noopener">10.1038/nrrheum.2011.68</a> (zuletzt aufgerufen am 3.11.2025).</li><li class="neutral-dark-grey-text-color">Singh-Grewal D, Schneider R, Bayer N et al.: Predictors of disease course and remission in systemic juvenile idiopathic arthritis: significance of early clinical and laboratory features. DOI: <a class="id-l
2024ink" href="https://doi.org/10.1002/art.21774" target="_blank" rel="noopener">10.1002/art.21774</a> (zuletzt aufgerufen am 3.11.2025).</li></ol> 2025 </div> 2026 2027 </div> 2028 2029 </div> 2030 2031 <div class="field field--name-field-mobile-slider field--type-boolean field--label-hidden field--layout"> 2032 2033 </div> 2034 2035 </div> 2036 </div> 2037 </div> 2038 2039 </div> 2040 2041 </div> 2042 </div> 2043 2044 </div> 2045 2046 </div> 2047</article> 2048 2049 </div> 2050 2051 2052 </section> 2053 </div> 2054 <div class="row content-container clearfix"> 2055 </div> 2056 </div> 2057 2058 </div> 2059 <footer class="site-footer"> 2060 <div class="site-footer__first container-fluid clearfix"> 2061 <div class="container"> 2062 <section class="row region region-footer-first"> 2063 <nav aria-labelledby="system-block-footercolumn1-menu" id="system-block-footercolumn1" data-block-plugin-id="system_menu_block:footer-column-1" class="block block-menu navigation menu--footer-column-1"> 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2450<script src="/sites/autoinflammation_de/files/js/js_kz6OI-jYWqmxaGcKYu84A6J1_pDlNV7iKkJWuRvcoOU.js?scope=footer&delta=0&language=de&theme=dolphin&include=eJx1kVtywyAMRTdEwpI0AjSEWkaMwG7c1Rccx5m26Y_EPTx0JZxIq02xgEPVJDayOORLbRunHI079zk5Rd3sSYwXFrVBl4J83YUJwuWWssWwYvYULpVQ_e3kr8tPwk1hFKNqaAEvMiXqaS6cxgv2HTR0b93d9Kx9SBNFIhM0jDb28Ftf8QPvP-FsGL82O4LJsqK2VOGw1ieSM6l9JKhehfnvqd1Id0CakXcFn6h5DO_RPGBJgEuTvQFqZP_hpqaxgCJl6f_B4qdq3zCzpkACNDsKMCG3RdEe-aCHuW820r48"></script>
vendor: 1 bytes, line 2450
2450
2451<script src="https://cdn.jsdelivr.net/gh/mattfarina/[email protected]/farbtastic.js"></script>
vendor: 1 bytes, line 2451
2451
2452<script src="/sites/autoinflammation_de/files/js/js_Nt06VhsQIK5qpa4YBkqrMRPcQIlOnHcLaEBMwcd04ww.js?scope=footer&delta=2&language=de&theme=dolphin&include=eJx1kVtywyAMRTdEwpI0AjSEWkaMwG7c1Rccx5m26Y_EPTx0JZxIq02xgEPVJDayOORLbRunHI079zk5Rd3sSYwXFrVBl4J83YUJwuWWssWwYvYULpVQ_e3kr8tPwk1hFKNqaAEvMiXqaS6cxgv2HTR0b93d9Kx9SBNFIhM0jDb28Ftf8QPvP-FsGL82O4LJsqK2VOGw1ieSM6l9JKhehfnvqd1Id0CakXcFn6h5DO_RPGBJgEuTvQFqZP_hpqaxgCJl6f_B4qdq3zCzpkACNDsKMCG3RdEe-aCHuW820r48"></script>
2452 2453 2454 2455
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Line numbers count LF bytes from the start of the resource, as the search results do. Vendor segments are library code the classifier recognised; they are stored but not indexed. Bytes are shown as Latin1 characters, one per byte.